Right sided aorta associated with tracheo-oesophageal fistula and oesophageal atresia.

Case 1 Born at 40 weeks gestation, weight 2.46 kg. Abnormalities-TOF (proximal atresia with distal fistula). TOF was repaired by ligation of the fistula and single layer interrupted nylon anastomosis of the proximal pouch and distal oesophagus on day one via a right thoracotomy at which a right sided aorta was recognised. Cardiac catheterization in the post-operative period showed right sided aortic arch with residual left aortic arch giving rise to the left subclavian artery, coarctation of right aortic arch with narrowing of anomalous right subclavian artery arising at the level of T4 from the right aortic arch. The child's IVP showed normal renal tracts and bladder. Vomiting in the first few weeks postoperatively was due to partial thoracic stomach demonstrated by barium swallow. The child is presently alive and well; and has had no cardiac surgery to date.